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Pharmacogenes

Genes that change drug response.

Reference for the pharmacogenes whose variants are clinically actionable in patients of African ancestry. Variant frequencies sourced from CPIC and gnomAD; clinical recommendations follow CPIC guidelines.

ADRB2

Beta-2 Adrenergic Receptor

Receptor for beta-2 agonists (albuterol, formoterol). Variants influence asthma response.

APOL1

Apolipoprotein L1

Variants are strongly associated with kidney disease risk.

CYP2C19

Cytochrome P450 2C19

Metabolizes clopidogrel, proton pump inhibitors, several SSRIs, and voriconazole. Variants determine whether drugs are activated or cleared at expected rates.

CYP2C9

Cytochrome P450 2C9

Co-metabolizes warfarin, NSAIDs, several oral hypoglycemics.

CYP2D6

Cytochrome P450 2D6

Metabolizes codeine, tramadol, tamoxifen, many antidepressants and antipsychotics. Phenotype ranges from poor to ultrarapid metabolizer.

DPYD

Dihydropyrimidine Dehydrogenase

Catabolizes 5-fluorouracil and capecitabine.

G6PD

Glucose-6-Phosphate Dehydrogenase

G6PD deficiency causes hemolytic anemia in response to certain medications (rasburicase, primaquine, dapsone, sulfa drugs).

HBB

Hemoglobin Subunit Beta

Mutations cause sickle cell disease (HbS), HbC, beta-thalassemia. Pharmacogenomic relevance: hydroxyurea response in SCD depends on HBB and modifier genes.

HLA-B

Major Histocompatibility Complex, Class I, B

Carrier status is associated with severe drug-hypersensitivity reactions to abacavir, allopurinol, and carbamazepine.

SLCO1B1

Solute Carrier Organic Anion Transporter Family Member 1B1

Transporter that controls statin uptake into liver.

TPMT

Thiopurine S-Methyltransferase

Metabolizes thiopurines (azathioprine, 6-mercaptopurine, thioguanine).

VKORC1

Vitamin K Epoxide Reductase Complex Subunit 1

The drug target for warfarin. Variants determine warfarin sensitivity.